Genes associated with “VEODS

41 genes foundOpen Targets: X-linked intellectual disability, van Esch type12 ClinVar P/LP variants
How are genes scored? (0–100 composite)
-5–15
ClinGen
0–15
HPO Freq
0–15
Open Targets
0–12
Phen2Gene
0–10
ClinVar
0–8
Constraint
0–8
Dosage
0–8
OMIM CS
0–8
PanelApp
0–5
OMIM
0–5
G2P
0–4
Breadth
Tiers:Strong Candidates (≥20)Consider (≥8)Possible (≥3)
Evidence dots:
HPOClinVarPhen2GeneOpen TargetsPanelApp
hover for details

Strong Candidates

1 gene
1
POLA1

DNA polymerase alpha 1, catalytic subunit

31
score
ClinGen: ModerateGTR ↑

Pigmentary disorder, reticulate, with systemic manifestations, X-linked

Frequency
-
P/LP Variants
12
OT Score
0.74

Consider

1 gene

VAN ESCH-O'DRISCOLL SYNDROME; VEODS

Possible

6 genes — click to expand

estrogen receptor 1

aminopeptidase puromycin sensitive

4HMGA2
Def

high mobility group AT-hook 2

4ALK
Def

ALK receptor tyrosine kinase

4WFS1
Def

wolframin ER transmembrane glycoprotein

4SGPL1
Def

sphingosine-1-phosphate lyase 1

Data aggregated from HPO/Monarch, ClinVar, OMIM (phenotypes + clinical synopsis), Open Targets, PanelApp, Phen2Gene, and Gene2Phenotype. Click a gene to view full details.