ZSWIM5

Chr 1

zinc finger SWIM-type containing 5

The ZSWIM5 protein is predicted to bind zinc ions and is located in the extracellular space. Mutations in this gene cause autosomal recessive intellectual disability with microcephaly and seizures, typically presenting in early childhood. The gene shows moderate constraint against loss-of-function variants (LOEUF 0.4), consistent with its role in neurodevelopment.

OMIMResearchSummary from RefSeq
LOEUF 0.40
Clinical SummaryZSWIM5
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.26) despite low pLI — interpret in context.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.40LOEUF
pLI 0.040
Z-score 5.10
OE 0.26 (0.170.40)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
2.32Z-score
OE missense 0.74 (0.690.80)
471 obs / 635.3 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.26 (0.170.40)
00.351.4
Missense OE0.74 (0.690.80)
00.61.4
Synonymous OE0.79
01.21.6
LoF obs/exp: 14 / 54.8Missense obs/exp: 471 / 635.3Syn Z: 2.68

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ZSWIM5 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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