ZNF510

Chr 9

zinc finger protein 510

This gene encodes a krueppel C2H2-type zinc-finger protein that may be involved in transcriptional regulation. Based on the extremely low pLI score, mutations in ZNF510 do not appear to cause haploinsufficient disease in humans. No established neurogenetic disorders have been definitively linked to ZNF510 mutations.

Summary from RefSeq, UniProt, Mechanism
0
Active trials
1
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.95
LOEUF
DN
Mechanism· predicted
Clinical SummaryZNF510
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.95LOEUF
pLI 0.000
Z-score 1.76
OE 0.61 (0.410.95)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.56Z-score
OE missense 0.91 (0.831.00)
310 obs / 338.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.61 (0.410.95)
00.351.4
Missense OE0.91 (0.831.00)
00.61.4
Synonymous OE1.05
01.21.6
LoF obs/exp: 15 / 24.4Missense obs/exp: 310 / 338.8Syn Z: -0.45
DN
0.93top 5%
GOF
0.85top 5%
LOF
0.1697th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ZNF510 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found