ZMYM1

Chr 1

zinc finger MYM-type containing 1

Also known as: MYM

The ZMYM1 protein enables protein dimerization and zinc ion binding in the nucleus. Mutations cause autosomal recessive developmental delay with dysmorphic facies and dental anomalies. This gene is highly constrained against loss-of-function variants, suggesting complete loss of function is likely incompatible with normal development.

ResearchSummary from RefSeq
DNmechanismLOEUF 0.66
Clinical SummaryZMYM1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.66LOEUF
pLI 0.000
Z-score 3.38
OE 0.46 (0.330.66)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
1.50Z-score
OE missense 0.82 (0.760.89)
460 obs / 560.0 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.46 (0.330.66)
00.351.4
Missense OE0.82 (0.760.89)
00.61.4
Synonymous OE0.95
01.21.6
LoF obs/exp: 21 / 45.6Missense obs/exp: 460 / 560.0Syn Z: 0.61
DN
0.6358th %ile
GOF
0.4381th %ile
LOF
0.3260th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ZMYM1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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