ZHX1-C8ORF76

Chr 8

ZHX1-C8orf76 readthrough

The ZHX1-C8ORF76 fusion protein results from natural read-through transcription between two neighboring genes and contains a distinct N-terminus from ZHX1 combined with C8ORF76 sequence. This gene is extremely tolerant to loss-of-function variants based on population data, and no definitive disease associations have been established for mutations in this fusion transcript. The clinical significance of variants in this read-through gene remains uncertain.

Summary from RefSeq
Research Assistant →
0
Active trials
0
Pubs (1 yr)
49
P/LP submissions
0%
P/LP missense
1.51
LOEUF
Mechanism
Clinical SummaryZHX1-C8ORF76
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
49 unique Pathogenic / Likely Pathogenic· 98 VUS of 155 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.51LOEUF
pLI 0.000
Z-score 0.10
OE 0.97 (0.641.51)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.04Z-score
OE missense 0.99 (0.861.14)
143 obs / 144.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.97 (0.641.51)
00.351.4
Missense OE0.99 (0.861.14)
00.61.4
Synonymous OE0.98
01.21.6
LoF obs/exp: 14 / 14.4Missense obs/exp: 143 / 144.3Syn Z: 0.14

ClinVar Variant Classifications

155 submitted variants in ClinVar

Classification Summary

Pathogenic49
VUS98
Likely Benign2
49
Pathogenic
98
VUS
2
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
49
0
49
Likely Pathogenic
0
0
0
0
0
VUS
0
97
1
0
98
Likely Benign
0
1
0
1
2
Benign
0
0
0
0
0
Total098501149

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

ZHX1-C8ORF76 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found