ZDHHC20

Chr 13

zDHHC palmitoyltransferase 20

Also known as: 4933421L13Rik, DHHC-20, DHHC20

ZDHHC20 encodes a palmitoyltransferase that catalyzes the addition of palmitate to cysteine residues in various protein substrates, including EGFR and CALHM1, thereby modulating protein localization and signaling. The gene shows low constraint to loss-of-function variants (pLI 0.0005, LOEUF 0.747), suggesting high tolerance to protein-truncating mutations. Disease associations and inheritance patterns for ZDHHC20 mutations have not been established in the provided data.

OMIMResearchSummary from RefSeq, UniProt
MultiplemechanismLOEUF 0.75
Clinical SummaryZDHHC20
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.75LOEUF
pLI 0.001
Z-score 2.43
OE 0.43 (0.260.75)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
1.25Z-score
OE missense 0.73 (0.630.85)
125 obs / 171.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.43 (0.260.75)
00.351.4
Missense OE0.73 (0.630.85)
00.61.4
Synonymous OE0.89
01.21.6
LoF obs/exp: 9 / 21.0Missense obs/exp: 125 / 171.1Syn Z: 0.69
DN
0.7228th %ile
GOF
0.77top 25%
LOF
0.2484th %ile

This gene has evidence for multiple mechanisms of pathogenicity (gain-of-function and dominant-negative). Both the Badonyi & Marsh prediction and the broader genomic evidence point to gain-of-function as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

GOFprediction above median
DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ZDHHC20 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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