YIF1B

Chr 19AR

Yip1 interacting factor homolog B, membrane trafficking protein

Also known as: FinGER8, KABAMAS

The protein functions in endoplasmic reticulum to Golgi vesicle transport and plays a key role in targeting receptors to neuronal dendrites and in primary cilium assembly. Biallelic mutations cause Kaya-Barakat-Masson syndrome, an autosomal recessive disorder. This gene is not highly constrained against loss-of-function variants.

OMIMResearchSummary from RefSeq, OMIM, UniProt
DNmechanismARLOEUF 1.101 OMIM phenotype
Clinical SummaryYIF1B
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Gene-Disease Validity (ClinGen)
Kaya-Barakat-Masson syndrome · ARDefinitive

Definitive — sufficient evidence for diagnostic panels

Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.10LOEUF
pLI 0.000
Z-score 1.29
OE 0.63 (0.381.10)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
1.40Z-score
OE missense 0.72 (0.630.83)
142 obs / 197.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.63 (0.381.10)
00.351.4
Missense OE0.72 (0.630.83)
00.61.4
Synonymous OE0.95
01.21.6
LoF obs/exp: 9 / 14.3Missense obs/exp: 142 / 197.5Syn Z: 0.37
DN
0.7132th %ile
GOF
0.5562th %ile
LOF
0.3746th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

YIF1B · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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