XAGE3

Chr X

X antigen family member 3

Also known as: CT12.3a, CT12.3b, GAGED4, PLAC6, XAGE-3, pp9012

The protein encoded by this gene belongs to the cancer-testis antigen family and is normally expressed in placenta and fetal tissues, where it may function in inhibiting cancer cell growth. XAGE3 is not currently associated with any established Mendelian disease or neurological phenotype. The gene shows tolerance to loss-of-function variants in the general population.

OMIMResearchSummary from RefSeq
MultiplemechanismLOEUF 1.31
Clinical SummaryXAGE3
Population Constraint (gnomAD)
Low constraint (pLI 0.09) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.31LOEUF
pLI 0.095
Z-score 1.17
OE 0.42 (0.171.31)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.58Z-score
OE missense 1.25 (1.001.58)
52 obs / 41.5 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.42 (0.171.31)
00.351.4
Missense OE1.25 (1.001.58)
00.61.4
Synonymous OE0.78
01.21.6
LoF obs/exp: 2 / 4.7Missense obs/exp: 52 / 41.5Syn Z: 0.65

This gene — mechanism propensity

DN
0.76top 25%
GOF
0.79top 25%
LOF
0.1499th %ile

This gene has evidence for multiple mechanisms of pathogenicity (gain-of-function and dominant-negative). Both the Badonyi & Marsh prediction and the broader genomic evidence point to gain-of-function as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

GOFprediction above median
DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

XAGE3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC