XAF1

Chr 17

XIAP associated factor 1

Also known as: BIRC4BP, HSXIAPAF1, XIAPAF1

The XAF1 protein functions as a negative regulator of inhibitor of apoptosis proteins (IAPs), promoting apoptosis by inhibiting anti-caspase activity and facilitating mitochondrial apoptosis pathway activation. This gene is not highly constrained against loss-of-function variants and is not currently associated with established Mendelian disease in pediatric populations. While XAF1 may function as a tumor suppressor, definitive pediatric neurogenetic disorders caused by XAF1 mutations have not been established.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 1.70
Clinical SummaryXAF1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
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Clinical Trials
1 active or recruiting trial — potential therapeutic options may be available

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.70LOEUF
pLI 0.000
Z-score -0.49
OE 1.14 (0.771.70)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.11Z-score
OE missense 0.98 (0.861.11)
161 obs / 164.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE1.14 (0.771.70)
00.351.4
Missense OE0.98 (0.861.11)
00.61.4
Synonymous OE1.08
01.21.6
LoF obs/exp: 16 / 14.0Missense obs/exp: 161 / 164.8Syn Z: -0.49

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

XAF1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold
Clinical Literature
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