WSCD1

Chr 17

WSC domain sialate O sulfotransferase 1

WSCD1 encodes a sialate:O-sulfotransferase that catalyzes 8-O-sulfation of sialic acid residues on glycolipids including GM1 gangliosides, functioning at the Golgi membrane. The gene is highly constrained against loss-of-function variants (pLI near 1.0), suggesting that mutations would likely cause severe developmental disorders. However, no specific human disease phenotypes have been definitively associated with WSCD1 mutations to date.

OMIMResearchSummary from RefSeq, UniProt
DNmechanismLOEUF 0.68
Clinical SummaryWSCD1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.68LOEUF
pLI 0.000
Z-score 2.88
OE 0.42 (0.270.68)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.54Z-score
OE missense 0.92 (0.841.01)
359 obs / 389.2 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.42 (0.270.68)
00.351.4
Missense OE0.92 (0.841.01)
00.61.4
Synonymous OE1.13
01.21.6
LoF obs/exp: 12 / 28.6Missense obs/exp: 359 / 389.2Syn Z: -1.28
DN
0.6454th %ile
GOF
0.5954th %ile
LOF
0.3163th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

WSCD1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found