WHR1

Chr 6

winged helix repair factor 1

Also known as: D6S60, D6S60E, G11, HLA-RP1, RP1, STK19, TWH19

This gene encodes a serine/threonine kinase which localizes predominantly to the nucleus. Its specific function is unknown; it is possible that phosphorylation of this protein is involved in transcriptional regulation. This gene localizes to the major histocompatibility complex (MHC) class III region on chromosome 6 and expresses two transcript variants. [provided by RefSeq, Jul 2008]

49
ClinVar variants
5
Pathogenic / LP
pLI score
0
Active trials
Clinical SummaryWHR1
📋
ClinVar Variants
5 Pathogenic / Likely Pathogenic· 40 VUS of 49 total submissions
Some data sources returned errors (1)

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

49 submitted variants in ClinVar

Classification Summary

Pathogenic4
Likely Pathogenic1
VUS40
Likely Benign3
Benign1
4
Pathogenic
1
Likely Pathogenic
40
VUS
3
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
4
0
4
Likely Pathogenic
0
0
1
0
1
VUS
0
38
2
0
40
Likely Benign
0
2
1
0
3
Benign
0
0
1
0
1
Total0409049

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

WHR1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

OMIM — Genotype-Phenotype Relationships

1 OMIM entry

Clinical Literature
Landmark / reviewRecent case evidence
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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