VWA3B

Chr 2AR

von Willebrand factor A domain containing 3B

Also known as: SCAR22

This gene encodes an intracellular protein that contains a von Willebrand factor type A domain. Intracellular proteins with VWA domains are thought to function in transcription, DNA repair, ribosomal and membrane transport and the proteasome. Mutations in this gene are associated with Spinocerebellar ataxia, autosomal recessive 22. Alternatively spliced transcript variants have been found for this gene. [provided by RefSeq, May 2017]

OMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

?Spinocerebellar ataxia, autosomal recessive 22MIM #616948
AR
0
Active trials
4
Pubs (1 yr)
P/LP submissions
P/LP missense
0.94
LOEUF
GOF
Mechanism· predicted

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.94LOEUF
pLI 0.000
Z-score 1.97
OE 0.75 (0.600.94)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
0.26Z-score
OE missense 0.97 (0.911.04)
678 obs / 697.2 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.75 (0.600.94)
00.351.4
Missense OE?0.97 (0.911.04)
00.61.4
Synonymous OE?0.97
01.21.6
LoF obs/exp: 52 / 69.7Missense obs/exp: 678 / 697.2Syn Z: 0.34

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

VWA3B · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →