VWA3A

Chr 16

von Willebrand factor A domain containing 3A

VWA3A encodes a protein predicted to be located in the extracellular region, though its specific function is not well characterized. Mutations cause a rare genetic condition with clinical features documented in GeneReviews, though the inheritance pattern and specific phenotypic details are not provided in the available data. The gene shows tolerance to loss-of-function variants based on constraint metrics.

OMIMResearchSummary from RefSeq
DNmechanismLOEUF 0.92
Clinical SummaryVWA3A
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.92LOEUF
pLI 0.000
Z-score 2.11
OE 0.72 (0.570.92)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.71Z-score
OE missense 0.92 (0.860.98)
581 obs / 631.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.72 (0.570.92)
00.351.4
Missense OE0.92 (0.860.98)
00.61.4
Synonymous OE0.84
01.21.6
LoF obs/exp: 49 / 67.7Missense obs/exp: 581 / 631.5Syn Z: 2.00
DN
0.6454th %ile
GOF
0.6150th %ile
LOF
0.3843th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

VWA3A · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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