VPS45

Chr 1

vacuolar protein sorting 45 homolog

Also known as: H1, H1VPS45, SCN5, VPS45A, VPS45B, VPS54A, VSP45, VSP45A

Vesicle mediated protein sorting plays an important role in segregation of intracellular molecules into distinct organelles. Genetic studies in yeast have identified more than 40 vacuolar protein sorting (VPS) genes involved in vesicle transport to vacuoles. This gene is a member of the Sec1 domain family, and shows a high degree of sequence similarity to mouse, rat and yeast Vps45. The exact function of this gene is not known, but its high expression in peripheral blood mononuclear cells suggests a role in trafficking proteins, including inflammatory mediators. Multiple alternatively spliced transcript variants have been found for this gene. [provided by RefSeq, Jul 2013]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtNeutropenia, severe congenital 5, autosomal recessive
0
Active trials
13
Pubs (1 yr)
P/LP submissions
P/LP missense
0.66
LOEUF
Mechanism
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.66LOEUF
pLI 0.000
Z-score 3.14
OE 0.43 (0.280.66)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
1.63Z-score
OE missense 0.74 (0.660.83)
229 obs / 309.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.43 (0.280.66)
00.351.4
Missense OE?0.74 (0.660.83)
00.61.4
Synonymous OE?0.79
01.21.6
LoF obs/exp: 15 / 35.1Missense obs/exp: 229 / 309.5Syn Z: 1.67

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

VPS45 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →