The protein is predicted to bind calcium ions and inhibit peptidases, with predicted roles in cellular responses and ovarian follicle development. This gene shows extremely low constraint against loss-of-function variants (pLI near zero), suggesting that complete loss of function may be well-tolerated. No established human disease associations have been reported for UMODL1 mutations.

Summary from RefSeq
Research Assistant →
0
Active trials
2
Pubs (1 yr)
85
P/LP submissions
0%
P/LP missense
1.12
LOEUF
Mechanism
Clinical SummaryUMODL1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
80 unique Pathogenic / Likely Pathogenic· 279 VUS of 427 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.12LOEUF
pLI 0.000
Z-score 0.73
OE 0.90 (0.731.12)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.32Z-score
OE missense 1.03 (0.971.09)
906 obs / 878.9 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.90 (0.731.12)
00.351.4
Missense OE1.03 (0.971.09)
00.61.4
Synonymous OE1.05
01.21.6
LoF obs/exp: 58 / 64.4Missense obs/exp: 906 / 878.9Syn Z: -0.82

ClinVar Variant Classifications

427 submitted variants in ClinVar

Classification Summary

Pathogenic78
Likely Pathogenic2
VUS279
Likely Benign43
Benign5
Conflicting1
78
Pathogenic
2
Likely Pathogenic
279
VUS
43
Likely Benign
5
Benign
1
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
78
0
78
Likely Pathogenic
0
0
2
0
2
VUS
0
274
5
0
279
Likely Benign
0
32
2
9
43
Benign
0
0
2
3
5
Conflicting
1
Total03068912408

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

UMODL1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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