ULK4

Chr 3

unc-51 like kinase 4

Also known as: FAM7C1, REC01035

This gene encodes a serine/threonine kinase that regulates cytoskeletal remodeling of alpha-tubulin, controlling neurite branching, elongation, and neuronal migration during development. Mutations cause neurodevelopmental disorders with intellectual disability and psychiatric manifestations including schizophrenia and bipolar disorder, with autosomal dominant inheritance. The gene is not highly constrained against loss-of-function variants, suggesting tolerance to such mutations.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 1.09
Clinical SummaryULK4
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
11 unique Pathogenic / Likely Pathogenic· 190 VUS of 296 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.09LOEUF
pLI 0.000
Z-score 0.88
OE 0.89 (0.721.09)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.91Z-score
OE missense 1.10 (1.031.17)
722 obs / 656.7 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.89 (0.721.09)
00.351.4
Missense OE1.10 (1.031.17)
00.61.4
Synonymous OE1.03
01.21.6
LoF obs/exp: 62 / 70.0Missense obs/exp: 722 / 656.7Syn Z: -0.41

ClinVar Variant Classifications

296 submitted variants in ClinVar

Classification Summary

Pathogenic7
Likely Pathogenic4
VUS190
Likely Benign38
Benign19
7
Pathogenic
4
Likely Pathogenic
190
VUS
38
Likely Benign
19
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
7
0
7
Likely Pathogenic
0
0
4
0
4
VUS
0
179
11
0
190
Likely Benign
1
16
8
13
38
Benign
0
10
5
4
19
Total12053517258

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

ULK4 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →