UGT2B4

Chr 4

UDP glucuronosyltransferase family 2 member B4

Also known as: HLUG25, UDPGT2B4, UDPGTH1, UDPGTh-1, UGT2B11

The UGT2B4 protein is a UDP-glucuronosyltransferase that conjugates lipophilic substrates with glucuronic acid to facilitate their excretion, playing an essential role in drug detoxification and metabolism of endogenous compounds including estrogen hormones. Mutations in UGT2B4 have not been established as a cause of human disease based on the available data. The gene shows low constraint against loss-of-function variants (LOEUF 1.22), suggesting tolerance to such mutations.

OMIMResearchSummary from RefSeq, UniProt
DNmechanismLOEUF 1.22
Clinical SummaryUGT2B4
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.22LOEUF
pLI 0.000
Z-score 0.84
OE 0.79 (0.531.22)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-1.15Z-score
OE missense 1.19 (1.091.31)
331 obs / 277.0 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.79 (0.531.22)
00.351.4
Missense OE1.19 (1.091.31)
00.61.4
Synonymous OE1.25
01.21.6
LoF obs/exp: 15 / 18.9Missense obs/exp: 331 / 277.0Syn Z: -1.93
DN
0.77top 25%
GOF
0.6149th %ile
LOF
0.2387th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

UGT2B4 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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