UGT2B15

Chr 4

UDP glucuronosyltransferase family 2 member B15

Also known as: HLUG4, UDPGT 2B8, UDPGT2B15, UDPGTH3, UGT2B8

This gene encodes UDP-glucuronosyltransferase 2B15, an enzyme that conjugates glucuronic acid to steroid hormones (testosterone, estradiol) and xenobiotic compounds to facilitate their elimination from the body. The gene shows very low constraint against loss-of-function variants (high LOEUF score), and no definitive disease associations have been established from the provided information. While UGT2B15 is important for detoxification and hormone metabolism, pathogenic variants causing pediatric neurologic disease are not documented in this dataset.

OMIMResearchSummary from RefSeq, UniProt
MultiplemechanismLOEUF 1.73
Clinical SummaryUGT2B15
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
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Clinical Trials
1 active or recruiting trial — potential therapeutic options may be available

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.73LOEUF
pLI 0.000
Z-score -1.20
OE 1.28 (0.941.73)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.87Z-score
OE missense 1.15 (1.051.26)
313 obs / 272.4 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE1.28 (0.941.73)
00.351.4
Missense OE1.15 (1.051.26)
00.61.4
Synonymous OE1.20
01.21.6
LoF obs/exp: 28 / 21.9Missense obs/exp: 313 / 272.4Syn Z: -1.55
DN
0.79top 25%
GOF
0.7028th %ile
LOF
0.2091th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

UGT2B15 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold
Clinical Literature
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