UBAP2

Chr 9

ubiquitin associated protein 2

Also known as: UBAP-2

This protein recruits ubiquitination machinery to RNA polymerase II for degradation when DNA repair fails and may promote degradation of ANXA2. Mutations cause autosomal recessive spastic paraplegia-80, characterized by progressive spasticity primarily affecting the lower limbs. The gene is highly intolerant to loss-of-function variants, indicating that complete loss of protein function is likely pathogenic.

ResearchSummary from RefSeq, UniProt
LOEUF 0.52
Clinical SummaryUBAP2
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.52LOEUF
pLI 0.000
Z-score 4.68
OE 0.36 (0.260.52)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
-0.11Z-score
OE missense 1.01 (0.951.08)
628 obs / 620.3 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.36 (0.260.52)
00.351.4
Missense OE1.01 (0.951.08)
00.61.4
Synonymous OE1.04
01.21.6
LoF obs/exp: 23 / 63.2Missense obs/exp: 628 / 620.3Syn Z: -0.50

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

UBAP2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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