TXNRD2

Chr 22

thioredoxin reductase 2

Also known as: GCCD5, SELZ, TR, TR-BETA, TR3, TRXR2, TXNR2

The protein encoded by this gene belongs to the pyridine nucleotide-disulfide oxidoreductase family, and is a member of the thioredoxin (Trx) system. Three thioredoxin reductase (TrxR) isozymes are found in mammals. TrxRs are selenocysteine-containing flavoenzymes, which reduce thioredoxins, as well as other substrates, and play a key role in redox homoeostasis. This gene encodes a mitochondrial form important for scavenging reactive oxygen species in mitochondria. It functions as a homodimer containing FAD, and selenocysteine (Sec) at the active site. Sec is encoded by UGA codon that normally signals translation termination. The 3' UTRs of selenoprotein mRNAs contain a conserved stem-loop structure, the Sec insertion sequence (SECIS) element, which is necessary for the recognition of UGA as a Sec codon rather than as a stop signal. Alternatively spliced transcript variants encoding different isoforms, including a few localized in the cytosol and some lacking the C-terminal Sec residue, have been found for this gene. [provided by RefSeq, Jun 2017]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtGlucocorticoid deficiency 5
1
Active trials
31
Pubs (1 yr)
P/LP submissions
P/LP missense
0.99
LOEUF
Multiple*
Mechanism· predicted
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GeneReview available — TXNRD2
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.99LOEUF
pLI 0.000
Z-score 1.60
OE 0.69 (0.490.99)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
0.64Z-score
OE missense 0.90 (0.820.99)
296 obs / 328.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.69 (0.490.99)
00.351.4
Missense OE?0.90 (0.820.99)
00.61.4
Synonymous OE?1.07
01.21.6
LoF obs/exp: 21 / 30.5Missense obs/exp: 296 / 328.5Syn Z: -0.60

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TXNRD2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.