TXNDC8

Chr 9

thioredoxin domain containing 8

Also known as: SPTRX-3, SPTRX3, TRX6, bA427L11.2

The protein is required for post-translational modifications of proteins involved in acrosomal biogenesis in sperm by reducing disulfide bonds. Mutations cause male infertility through a dominant-negative mechanism. The gene shows tolerance to loss-of-function variants, consistent with its role in reproductive rather than essential cellular functions.

OMIMResearchSummary from RefSeq, UniProt, Mechanism
MultiplemechanismLOEUF 1.32
Clinical SummaryTXNDC8
Population Constraint (gnomAD)
Low constraint (pLI 0.01) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
34 unique Pathogenic / Likely Pathogenic· 20 VUS of 56 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.32LOEUF
pLI 0.008
Z-score 1.01
OE 0.58 (0.291.32)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.41Z-score
OE missense 1.15 (0.941.40)
70 obs / 61.0 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.58 (0.291.32)
00.351.4
Missense OE1.15 (0.941.40)
00.61.4
Synonymous OE1.00
01.21.6
LoF obs/exp: 4 / 6.9Missense obs/exp: 70 / 61.0Syn Z: -0.00
DN
0.82top 10%
GOF
0.7028th %ile
LOF
0.1895th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

56 submitted variants in ClinVar

Classification Summary

Pathogenic29
Likely Pathogenic5
VUS20
Likely Benign2
29
Pathogenic
5
Likely Pathogenic
20
VUS
2
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
29
0
29
Likely Pathogenic
0
0
5
0
5
VUS
0
18
2
0
20
Likely Benign
0
1
1
0
2
Benign
0
0
0
0
0
Total01937056

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

TXNDC8 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC