TULP3

Chr 12AR

TUB like protein 3

Also known as: HRCDF, TUBL3

This gene encodes a member of the tubby gene family of bipartite transcription factors. Members of this family have been identified in plants, vertebrates, and invertebrates, and they share a conserved N-terminal transcription activation region and a conserved C-terminal DNA and phosphatidylinositol-phosphate binding region. The encoded protein binds to phosphoinositides in the plasma membrane via its C-terminal region and probably functions as a membrane-bound transcription regulator that translocates to the nucleus in response to phosphoinositide hydrolysis, for instance, induced by G-protein-coupled-receptor signaling. It plays an important role in neuronal development and function. Two transcript variants encoding distinct isoforms have been identified for this gene. [provided by RefSeq, May 2009]

OMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

Hepatorenocardiac degenerative fibrosisMIM #619902
AR

Clinical highlights

Gene-disease validity (ClinGen)
ciliopathy · ARStrongappropriate for clinical testing
0
Active trials
16
Pubs (1 yr)
P/LP submissions
P/LP missense
0.88
LOEUF
DN
Mechanism· predicted

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.88LOEUF
pLI 0.000
Z-score 2.01
OE 0.55 (0.360.88)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
0.26Z-score
OE missense 0.96 (0.871.06)
283 obs / 295.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.55 (0.360.88)
00.351.4
Missense OE?0.96 (0.871.06)
00.61.4
Synonymous OE?1.06
01.21.6
LoF obs/exp: 13 / 23.5Missense obs/exp: 283 / 295.4Syn Z: -0.48

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TULP3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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