TUFM

Chr 16

Tu translation elongation factor, mitochondrial

Also known as: COXPD4, EF-TuMT, EFTU, P43

This gene encodes a protein which participates in protein translation in mitochondria. Mutations in this gene have been associated with combined oxidative phosphorylation deficiency resulting in lactic acidosis and fatal encephalopathy. A pseudogene has been identified on chromosome 17. [provided by RefSeq, Jul 2008]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtCombined oxidative phosphorylation deficiency 4

Clinical highlights

Gene-disease validity (ClinGen)
mitochondrial disease · ARModerateconsider for supplementary testing
0
Active trials
38
Pubs (1 yr)
P/LP submissions
P/LP missense
0.74
LOEUF
Multiple*
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.74LOEUF
pLI 0.004
Z-score 2.37
OE 0.39 (0.220.74)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
1.40Z-score
OE missense 0.76 (0.680.85)
205 obs / 269.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.39 (0.220.74)
00.351.4
Missense OE?0.76 (0.680.85)
00.61.4
Synonymous OE?0.99
01.21.6
LoF obs/exp: 7 / 17.8Missense obs/exp: 205 / 269.5Syn Z: 0.09

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TUFM · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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