TUBGCP3

Chr 13

tubulin gamma complex component 3

The TUBGCP3 protein is a component of the gamma-tubulin ring complex that mediates microtubule nucleation, which is critical for centrosome duplication and spindle formation during cell division. Mutations cause microcephaly and chorioretinopathy, autosomal recessive, an early-onset disorder affecting brain development and the retina. This gene is highly constrained against loss-of-function variants (LOEUF 0.35), reflecting its essential role in cellular processes.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.35
Clinical SummaryTUBGCP3
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.22) despite low pLI — interpret in context.
Some data sources returned errors (1)

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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.35LOEUF
pLI 0.455
Z-score 5.50
OE 0.22 (0.140.35)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
2.52Z-score
OE missense 0.69 (0.630.75)
353 obs / 513.4 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.22 (0.140.35)
00.351.4
Missense OE0.69 (0.630.75)
00.61.4
Synonymous OE0.93
01.21.6
LoF obs/exp: 13 / 58.4Missense obs/exp: 353 / 513.4Syn Z: 0.76

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TUBGCP3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC