TUBB3

Chr 16

tubulin beta 3 class III

Also known as: CDCBM, CDCBM1, CFEOM3, CFEOM3A, CFEOM3A1, FEOM3, TUBB4, beta-4

This gene encodes a class III member of the beta tubulin protein family. Beta tubulins are one of two core protein families (alpha and beta tubulins) that heterodimerize and assemble to form microtubules. This protein is primarily expressed in neurons and may be involved in neurogenesis and axon guidance and maintenance. Mutations in this gene are the cause of congenital fibrosis of the extraocular muscles type 3. Alternate splicing results in multiple transcript variants. A pseudogene of this gene is found on chromosome 6. [provided by RefSeq, Oct 2010]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtFibrosis of extraocular muscles, congenital, 3A
UniProtCortical dysplasia, complex, with other brain malformations 1

Clinical highlights

Gene-disease validity (ClinGen)
TUBB3-related tubulinopathy · ADDefinitivesufficient evidence for diagnostic panels
2
Active trials
118
Pubs (1 yr)
P/LP submissions
P/LP missense
1.11
LOEUF
DN
Mechanism· predicted
📖
GeneReview available — TUBB3
Authoritative clinical overview · Recommended first read
Open GeneReview ↗
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.11LOEUF
pLI 0.000
Z-score 1.13
OE 0.75 (0.521.11)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
1.78Z-score
OE missense 0.78 (0.720.85)
400 obs / 513.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.75 (0.521.11)
00.351.4
Missense OE?0.78 (0.720.85)
00.61.4
Synonymous OE?1.30
01.21.6
LoF obs/exp: 18 / 24.0Missense obs/exp: 400 / 513.8Syn Z: -3.73

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TUBB3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

VCEP specificationsBrain MalformationsReleased
Specifications ↗Panel ↗