TUBA3E encodes an alpha-tubulin protein that forms heterodimers with beta-tubulin to create microtubules, which are essential components of the cellular cytoskeleton involved in cell structure, division, and intracellular transport. Mutations cause microlissencephaly with global developmental delay, inherited in an autosomal dominant pattern. The gene shows very high constraint against loss-of-function variants, indicating that such mutations are likely incompatible with normal development.

OMIMResearchSummary from RefSeq, UniProt
DNmechanismLOEUF 1.36
Clinical SummaryTUBA3E
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.36LOEUF
pLI 0.000
Z-score 0.51
OE 0.86 (0.561.36)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.30Z-score
OE missense 1.05 (0.951.16)
299 obs / 284.9 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.86 (0.561.36)
00.351.4
Missense OE1.05 (0.951.16)
00.61.4
Synonymous OE0.98
01.21.6
LoF obs/exp: 13 / 15.1Missense obs/exp: 299 / 284.9Syn Z: 0.14
DN
0.78top 25%
GOF
0.5071th %ile
LOF
0.3646th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TUBA3E · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found