TRPM1

Chr 15AR

transient receptor potential cation channel subfamily M member 1

Also known as: CSNB1C, LTRPC1, MLSN1

This gene encodes TRPM1, a constitutively open calcium-permeable cation channel that plays an essential role in the depolarizing photoresponse of retinal ON bipolar cells by mediating calcium and other divalent cation influx. Mutations cause autosomal recessive complete congenital stationary night blindness-1C, a condition present from birth affecting night vision. The gene shows very low constraint against loss-of-function variants (pLI near zero), consistent with its recessive inheritance pattern.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 1.071 OMIM phenotype
Clinical SummaryTRPM1
🧬
Gene-Disease Validity (ClinGen)
TRPM1-related retinopathy · ARDefinitive

Definitive — sufficient evidence for diagnostic panels

Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.07LOEUF
pLI 0.000
Z-score 1.03
OE 0.88 (0.721.07)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.13Z-score
OE missense 1.01 (0.961.07)
914 obs / 903.0 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.88 (0.721.07)
00.351.4
Missense OE1.01 (0.961.07)
00.61.4
Synonymous OE1.07
01.21.6
LoF obs/exp: 70 / 80.0Missense obs/exp: 914 / 903.0Syn Z: -0.98
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
definitiveTRPM1-related night blindness, congenital stationaryLOFAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.6357th %ile
GOF
0.75top 25%
LOF
0.3941th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TRPM1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 5 full-text resultsSearch PubTator3 ↗