TRMT44

Chr 4

tRNA methyltransferase 44 homolog

Also known as: C4orf23, METTL19, TRM44

This gene encodes a tRNA methyltransferase that modifies uracil bases in tRNA using S-adenosyl-L-methionine as a methyl donor. Mutations may cause partial epilepsy with pericentral spikes, though this association has not been definitively established. The gene shows minimal constraint against loss-of-function variants, suggesting tolerance to such mutations.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
0
Pubs (1 yr)
75
P/LP submissions
0%
P/LP missense
1.36
LOEUF
Mechanism
Clinical SummaryTRMT44
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
75 unique Pathogenic / Likely Pathogenic· 160 VUS of 272 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.36LOEUF
pLI 0.000
Z-score -0.08
OE 1.01 (0.771.36)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.85Z-score
OE missense 1.12 (1.041.21)
454 obs / 405.6 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE1.01 (0.771.36)
00.351.4
Missense OE1.12 (1.041.21)
00.61.4
Synonymous OE1.01
01.21.6
LoF obs/exp: 33 / 32.5Missense obs/exp: 454 / 405.6Syn Z: -0.14

ClinVar Variant Classifications

272 submitted variants in ClinVar

Classification Summary

Pathogenic72
Likely Pathogenic3
VUS160
Likely Benign14
72
Pathogenic
3
Likely Pathogenic
160
VUS
14
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
72
0
72
Likely Pathogenic
0
0
3
0
3
VUS
0
144
16
0
160
Likely Benign
0
11
2
1
14
Benign
0
0
0
0
0
Total0155931249

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

TRMT44 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found