TRMT1L

Chr 1

tRNA methyltransferase 1L

Also known as: C1orf25, MST070, MSTP070, TRM1L, bG120K12.3

This gene encodes a protein that has some similarity to N2,N2-dimethylguanosine tRNA methyltransferase from other organisms. Studies of the mouse ortholog have shown that this protein plays a role in motor coordination and exploratory behavior, and it may also be involved in modulating postnatal neuronal functions. Alternatively spliced transcripts have been identified for this gene. [provided by RefSeq, Jan 2011]

OMIMResearchGenerating clinical summary…
LOFmechanismLOEUF 0.36
Clinical SummaryTRMT1L
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.80) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint?
0.36LOEUF
pLI 0.797
Z-score 4.48
OE 0.19 (0.110.36)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint?
1.86Z-score
OE missense 0.73 (0.660.81)
275 obs / 376.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.19 (0.110.36)
00.351.4
Missense OE?0.73 (0.660.81)
00.61.4
Synonymous OE?0.88
01.21.6
LoF obs/exp: 7 / 36.1Missense obs/exp: 275 / 376.7Syn Z: 1.09

This gene — mechanism propensity

DN
0.4091th %ile
GOF
0.2298th %ile
LOF
0.65top 25%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.36

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TRMT1L · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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