TRMT12

Chr 8

tRNA methyltransferase 12 homolog

S-adenosyl-L-methionine-dependent transferase that acts as a component of the wybutosine biosynthesis pathway. Wybutosine is a hyper modified guanosine with a tricyclic base found at the 3'-position adjacent to the anticodon of eukaryotic phenylalanine tRNA. Catalyzes the transfer of the alpha-amino-alpha-carboxypropyl (acp) group from S-adenosyl-L-methionine to the C-7 position of 4-demethylwyosine (imG-14) to produce wybutosine-86

0
Active trials
1
Pubs (1 yr)
21
P/LP submissions
0%
P/LP missense
0.53
LOEUF
Mechanism
Clinical SummaryTRMT12
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.23) despite low pLI — interpret in context.
📋
ClinVar Variants
21 unique Pathogenic / Likely Pathogenic· 41 VUS of 65 total submissions
Some data sources returned errors (1)

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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.53LOEUF
pLI 0.326
Z-score 2.96
OE 0.23 (0.110.53)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
0.15Z-score
OE missense 0.97 (0.871.08)
230 obs / 236.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.23 (0.110.53)
00.351.4
Missense OE0.97 (0.871.08)
00.61.4
Synonymous OE1.01
01.21.6
LoF obs/exp: 4 / 17.2Missense obs/exp: 230 / 236.6Syn Z: -0.11

ClinVar Variant Classifications

65 submitted variants in ClinVar

Classification Summary

Pathogenic21
VUS41
Likely Benign3
21
Pathogenic
41
VUS
3
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
21
0
21
Likely Pathogenic
0
0
0
0
0
VUS
0
35
6
0
41
Likely Benign
0
2
1
0
3
Benign
0
0
0
0
0
Total03728065

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

TRMT12 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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