TRIQK

Chr 8

triple QxxK/R motif containing

Also known as: C8orf83, PRO0845, UPF0599

The TRIQK protein is predicted to localize to the endoplasmic reticulum membrane and may function in cell growth and maintenance of cell morphology. This gene shows low constraint against loss-of-function variants (pLI 0.01, LOEUF 1.76), but no specific diseases have been definitively associated with TRIQK mutations in the current literature. The clinical significance of variants in this gene remains to be established.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
0
Pubs (1 yr)
38
P/LP submissions
0%
P/LP missense
1.76
LOEUF
DN
Mechanism· predicted
Clinical SummaryTRIQK
Population Constraint (gnomAD)
Low constraint (pLI 0.01) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
38 unique Pathogenic / Likely Pathogenic· 16 VUS of 61 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.76LOEUF
pLI 0.010
Z-score 0.35
OE 0.80 (0.361.76)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.19Z-score
OE missense 0.91 (0.681.23)
31 obs / 34.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.80 (0.361.76)
00.351.4
Missense OE0.91 (0.681.23)
00.61.4
Synonymous OE1.06
01.21.6
LoF obs/exp: 3 / 3.7Missense obs/exp: 31 / 34.1Syn Z: -0.16
DN
0.6745th %ile
GOF
0.5856th %ile
LOF
0.2484th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

61 submitted variants in ClinVar

Classification Summary

Pathogenic37
Likely Pathogenic1
VUS16
Likely Benign1
37
Pathogenic
1
Likely Pathogenic
16
VUS
1
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
37
0
37
Likely Pathogenic
0
0
1
0
1
VUS
0
15
1
0
16
Likely Benign
0
0
1
0
1
Benign
0
0
0
0
0
Total01540055

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

TRIQK · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC