TPM2

Chr 9

tropomyosin 2

Also known as: AMCD1, CMYO23, CMYP23, DA1, DA2B, DA2B4, HEL-S-273, NEM4

This gene encodes beta-tropomyosin, a member of the actin filament binding protein family, and mainly expressed in slow, type 1 muscle fibers. Mutations in this gene can alter the expression of other sarcomeric tropomyosin proteins, and cause cap disease, nemaline myopathy and distal arthrogryposis syndromes. Alternatively spliced transcript variants encoding different isoforms have been found for this gene.[provided by RefSeq, Mar 2009]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtCongenital myopathy 23
UniProtArthrogryposis, distal, 1A
UniProtArthrogryposis, distal, 2B4

Clinical highlights

Gene-disease validity (ClinGen)
TPM2-related myopathy · ADDefinitivesufficient evidence for diagnostic panels
0
Active trials
46
Pubs (1 yr)
P/LP submissions
P/LP missense
0.83
LOEUF
Multiple*
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.83LOEUF
pLI 0.000
Z-score 2.12
OE 0.47 (0.280.83)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
2.13Z-score
OE missense 0.52 (0.430.62)
80 obs / 154.7 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios?
LoF OE?0.47 (0.280.83)
00.351.4
Missense OE?0.52 (0.430.62)
00.61.4
Synonymous OE?1.03
01.21.6
LoF obs/exp: 9 / 19.0Missense obs/exp: 80 / 154.7Syn Z: -0.19

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TPM2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →