TOP1MT

Chr 8

DNA topoisomerase I mitochondrial

This gene encodes a mitochondrial DNA topoisomerase that plays a role in the modification of DNA topology. The encoded protein is a type IB topoisomerase and catalyzes the transient breaking and rejoining of DNA to relieve tension and DNA supercoiling generated in the mitochondrial genome during replication and transcription. Alternatively spliced transcript variants encoding multiple isoforms have been observed for this gene. [provided by RefSeq, May 2012]

0
Active trials
8
Pubs (1 yr)
0
P/LP submissions
P/LP missense
1.68
LOEUF
Mechanism
Clinical SummaryTOP1MT
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.68LOEUF
pLI 0.000
Z-score -1.70
OE 1.31 (1.031.68)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.11Z-score
OE missense 1.02 (0.931.10)
393 obs / 386.9 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE1.31 (1.031.68)
00.351.4
Missense OE1.02 (0.931.10)
00.61.4
Synonymous OE0.99
01.21.6
LoF obs/exp: 45 / 34.3Missense obs/exp: 393 / 386.9Syn Z: 0.13

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TOP1MT · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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