TNFSF12

Chr 17

TNF superfamily member 12

Also known as: APO3L, DR3LG, TNF12, TNLG4A, TWEAK

The protein encoded by this gene is a cytokine that belongs to the tumor necrosis factor (TNF) ligand family. This protein is a ligand for the FN14/TWEAKR receptor. This cytokine has overlapping signaling functions with TNF, but displays a much wider tissue distribution. This cytokine, which exists in both membrane-bound and secreted forms, can induce apoptosis via multiple pathways of cell death in a cell type-specific manner. This cytokine is also found to promote proliferation and migration of endothelial cells, and thus acts as a regulator of angiogenesis. Alternative splicing results in multiple transcript variants. Some transcripts skip the last exon of this gene and continue into the second exon of the neighboring TNFSF13 gene; such read-through transcripts are contained in GeneID 407977, TNFSF12-TNFSF13. [provided by RefSeq, Oct 2010]

3
Active trials
21
Pathogenic / LP
305
ClinVar variants
39
Pubs (1 yr)
1.0
Missense Z
0.41
LOEUF
Clinical SummaryTNFSF12
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Gene-Disease Validity (ClinGen)
common variable immunodeficiency · ADLimited

Limited evidence — not for standalone diagnostic reporting

Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.77) — some intolerance to loss-of-function variants.
📋
ClinVar Variants
21 Pathogenic / Likely Pathogenic· 163 VUS of 305 total submissions
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Clinical Trials
3 active or recruiting trials — potential therapeutic options may be available

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.41LOEUF
pLI 0.770
Z-score 3.60
OE 0.18 (0.090.41)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
0.98Z-score
OE missense 0.79 (0.690.91)
137 obs / 173.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.18 (0.090.41)
00.351.4
Missense OE0.79 (0.690.91)
00.61.4
Synonymous OE1.05
01.21.6
LoF obs/exp: 4 / 22.4Missense obs/exp: 137 / 173.4Syn Z: -0.33

ClinVar Variant Classifications

305 submitted variants in ClinVar

Classification Summary

Pathogenic20
Likely Pathogenic1
VUS163
Likely Benign108
Benign12
Conflicting1
20
Pathogenic
1
Likely Pathogenic
163
VUS
108
Likely Benign
12
Benign
1
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
20
0
20
Likely Pathogenic
0
0
1
0
1
VUS
4
128
29
2
163
Likely Benign
0
0
42
66
108
Benign
0
0
6
6
12
Conflicting
1
Total41289874305

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

TNFSF12 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Literature
Landmark / reviewRecent case evidence