TMEM249

Chr 8

catsper channel auxiliary subunit theta

Also known as: C8ORFK29, TMEM249

The protein is an auxiliary component of the CatSper complex that is involved in sperm cell hyperactivation and is predicted to be located in the sperm principal piece. Based on the available data, no human diseases have been definitively associated with TMEM249 mutations. The gene shows moderate tolerance to loss-of-function variants (pLI 0.10, LOEUF 0.85), suggesting it may not be highly constrained in humans.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
1
Pubs (1 yr)
24
P/LP submissions
P/LP missense
0.85
LOEUF
DN
Mechanism· predicted
Clinical SummaryTMEM249
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.33) despite low pLI — interpret in context.
📋
ClinVar Variants
24 unique Pathogenic / Likely Pathogenic· 10 VUS of 36 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.85LOEUF
pLI 0.105
Z-score 1.88
OE 0.33 (0.150.85)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.88Z-score
OE missense 0.80 (0.690.93)
120 obs / 150.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.33 (0.150.85)
00.351.4
Missense OE0.80 (0.690.93)
00.61.4
Synonymous OE1.05
01.21.6
LoF obs/exp: 3 / 9.1Missense obs/exp: 120 / 150.6Syn Z: -0.31
DN
0.6648th %ile
GOF
0.6149th %ile
LOF
0.3065th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

36 submitted variants in ClinVar

Classification Summary

Pathogenic22
Likely Pathogenic2
VUS10
Likely Benign1
Benign1
22
Pathogenic
2
Likely Pathogenic
10
VUS
1
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
22
Likely Pathogenic
2
VUS
10
Likely Benign
1
Benign
1
Total36

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

TMEM249 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found