TMEM219

Chr 16

transmembrane protein 219

Also known as: IGFBP-3R, IGFBP3R

The protein functions as a cell death receptor that specifically binds IGFBP3 and may mediate caspase-8-dependent apoptosis. This gene is extremely intolerant to loss-of-function variants (pLI = 0.0001), suggesting that mutations would likely cause severe developmental disorders, though specific associated diseases have not yet been established. The inheritance pattern for potential TMEM219-related disorders has not been determined.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 1.47
Clinical SummaryTMEM219
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.47LOEUF
pLI 0.000
Z-score 0.58
OE 0.79 (0.451.47)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.24Z-score
OE missense 0.94 (0.811.09)
126 obs / 133.9 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.79 (0.451.47)
00.351.4
Missense OE0.94 (0.811.09)
00.61.4
Synonymous OE0.93
01.21.6
LoF obs/exp: 7 / 8.9Missense obs/exp: 126 / 133.9Syn Z: 0.44

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TMEM219 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 3 full-text resultsSearch PubTator3 ↗