TLN1

Chr 9

talin 1

Also known as: ILWEQ, TLN, talin-1

Talin-1 is a high molecular weight cytoskeletal protein that connects major cytoskeletal structures to the plasma membrane and organizes cortical microtubule stabilizing complexes at focal adhesions. Mutations cause autosomal recessive limb-girdle muscular dystrophy type 2R, characterized by progressive proximal muscle weakness typically beginning in childhood or adolescence. This gene is highly constrained against loss-of-function variants in the general population.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.13
Clinical SummaryTLN1
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 1.00). One damaged copy is likely sufficient to cause disease.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Dual constrained — LoF & missense intolerant
LoF Constraint
0.13LOEUF
pLI 1.000
Z-score 9.84
OE 0.08 (0.050.13)
Highly constrained

Among the most LoF-intolerant genes (~top 3%)

Missense Constraint
4.67Z-score
OE missense 0.66 (0.620.69)
970 obs / 1475.0 exp
Constrained

Highly missense-constrained (top ~0.1%)

Observed / Expected Ratios
LoF OE0.08 (0.050.13)
00.351.4
Missense OE0.66 (0.620.69)
00.61.4
Synonymous OE0.92
01.21.6
LoF obs/exp: 10 / 132.1Missense obs/exp: 970 / 1475.0Syn Z: 1.47

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TLN1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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