THBS2

Chr 6AD

thrombospondin 2

Also known as: EDSCLL3, TSP2

The protein is an adhesive glycoprotein that mediates cell-to-cell and cell-to-matrix interactions and functions as an inhibitor of angiogenesis. Mutations cause Ehlers-Danlos syndrome, classic-like type 3, which primarily affects connective tissue and increases susceptibility to lumbar disc herniation. The gene is inherited in an autosomal dominant pattern and is highly constrained against loss-of-function variants.

OMIMResearchSummary from RefSeq, OMIM, UniProt
ADLOEUF 0.352 OMIM phenotypes
Clinical SummaryTHBS2
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.56) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.35LOEUF
pLI 0.556
Z-score 5.58
OE 0.22 (0.140.35)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
2.21Z-score
OE missense 0.77 (0.720.83)
587 obs / 758.7 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.22 (0.140.35)
00.351.4
Missense OE0.77 (0.720.83)
00.61.4
Synonymous OE1.02
01.21.6
LoF obs/exp: 13 / 59.5Missense obs/exp: 587 / 758.7Syn Z: -0.25

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

THBS2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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