THAP6 encodes a DNA-binding transcription factor that regulates gene transcription and endothelial cell proliferation. The gene shows very low constraint against loss-of-function variants (pLI 0.0006), and no definitive disease associations have been established in humans. Currently, there is insufficient evidence to determine specific neurological phenotypes or inheritance patterns associated with THAP6 variants.

OMIMResearchSummary from RefSeq
DNmechanismLOEUF 1.33
Clinical SummaryTHAP6
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.33LOEUF
pLI 0.001
Z-score 0.89
OE 0.68 (0.371.33)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.35Z-score
OE missense 0.91 (0.781.07)
109 obs / 119.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.68 (0.371.33)
00.351.4
Missense OE0.91 (0.781.07)
00.61.4
Synonymous OE0.98
01.21.6
LoF obs/exp: 6 / 8.8Missense obs/exp: 109 / 119.8Syn Z: 0.10
DN
0.7132th %ile
GOF
0.5171th %ile
LOF
0.2776th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

THAP6 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found