TGM5

Chr 15AR

transglutaminase 5

Also known as: PSS2, TG(X), TGASE5, TGASEX, TGMX, TGX

The encoded protein is a transglutaminase that catalyzes calcium-dependent cross-linking of proteins and contributes to cornified cell envelope formation in keratinocytes. Mutations cause peeling skin syndrome 2, an autosomal recessive disorder affecting skin integrity. The gene shows tolerance to loss-of-function variants (LOEUF 1.436), consistent with the recessive inheritance pattern.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 1.441 OMIM phenotype
Clinical SummaryTGM5
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.44LOEUF
pLI 0.000
Z-score -0.47
OE 1.09 (0.831.44)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.32Z-score
OE missense 1.05 (0.961.14)
403 obs / 385.5 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE1.09 (0.831.44)
00.351.4
Missense OE1.05 (0.961.14)
00.61.4
Synonymous OE0.93
01.21.6
LoF obs/exp: 36 / 33.1Missense obs/exp: 403 / 385.5Syn Z: 0.69

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TGM5 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →