TEX30

Chr 13

testis expressed 30

Also known as: C13orf27

The TEX30 protein is a testis-expressed gene involved in spermatogenesis and male fertility. Mutations cause primary ciliary dyskinesia with male infertility, a condition affecting respiratory cilia function and sperm motility that follows autosomal recessive inheritance. The gene shows low constraint against loss-of-function variants, consistent with its recessive disease mechanism.

DNmechanismLOEUF 1.31
Clinical SummaryTEX30
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.31LOEUF
pLI 0.001
Z-score 0.93
OE 0.67 (0.361.31)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.36Z-score
OE missense 0.91 (0.771.07)
106 obs / 116.9 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.67 (0.361.31)
00.351.4
Missense OE0.91 (0.771.07)
00.61.4
Synonymous OE0.75
01.21.6
LoF obs/exp: 6 / 9.0Missense obs/exp: 106 / 116.9Syn Z: 1.24
DN
0.6745th %ile
GOF
0.4283th %ile
LOF
0.3164th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TEX30 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →