The protein is a component of the transverse central element of synaptonemal complexes that form between homologous chromosomes during meiotic prophase and requires SYCP1 for incorporation into the central element. Mutations cause autosomal recessive male infertility due to meiotic arrest. The gene is not highly constrained in the general population, consistent with its specialized role in male reproductive function.

Summary from RefSeq, UniProt
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0
Active trials
3
Pubs (1 yr)
0
P/LP submissions
P/LP missense
1.78
LOEUF
Multiple*
Mechanism· predicted
Clinical SummaryTEX12
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.78LOEUF
pLI 0.000
Z-score 0.09
OE 0.96 (0.491.78)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.30Z-score
OE missense 0.89 (0.711.12)
51 obs / 57.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.96 (0.491.78)
00.351.4
Missense OE0.89 (0.711.12)
00.61.4
Synonymous OE0.98
01.21.6
LoF obs/exp: 5 / 5.2Missense obs/exp: 51 / 57.3Syn Z: 0.06
DN
0.6937th %ile
GOF
0.6541th %ile
LOF
0.3454th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TEX12 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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