TCHHL1

Chr 1

trichohyalin like 1

Also known as: S100A17, THHL1

This gene belongs to the S100 fused-type protein (SFTP) gene family, and is located in a cluster of SFTP genes on chromosome 1q21. Several members of this family have been implicated in the development of complex skin disorders. This gene is evolutionarily conserved; its expression appears to be hair-specific and spatially restricted within the distal inner root sheath of the hair follicle. It thus may have an important role in hair morphogenesis. [provided by RefSeq, Aug 2013]

ResearchGenerating clinical summary…
LOEUF 1.07
Clinical SummaryTCHHL1
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.58) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint?
1.07LOEUF
pLI 0.584
Z-score 1.53
OE 0.00 (0.001.07)
Moderately constrained

Highly tolerant — LoF variants common in population

Missense Constraint?
-0.54Z-score
OE missense 1.07 (0.991.16)
460 obs / 428.7 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.00 (0.001.07)
00.351.4
Missense OE?1.07 (0.991.16)
00.61.4
Synonymous OE?1.20
01.21.6
LoF obs/exp: 0 / 2.7Missense obs/exp: 460 / 428.7Syn Z: -1.98

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TCHHL1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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