TCEAL9

Chr X

transcription elongation factor A like 9

Also known as: WBP5, WEX6

This protein contains a WW domain that mediates protein-protein interactions through binding polyproline ligands and may be involved in transcriptional regulation. Mutations in TCEAL9 have not been definitively associated with human disease based on the provided information. The gene shows tolerance to loss-of-function variants with a low pLI score (0.12) and high LOEUF score (1.82).

Summary from RefSeq, UniProt
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0
Active trials
0
Pubs (1 yr)
0
P/LP submissions
P/LP missense
1.82
LOEUF
Multiple*
Mechanism· predicted
Clinical SummaryTCEAL9
Population Constraint (gnomAD)
Low constraint (pLI 0.12) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.82LOEUF
pLI 0.122
Z-score 0.43
OE 0.63 (0.201.82)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.24Z-score
OE missense 0.89 (0.671.19)
32 obs / 36.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.63 (0.201.82)
00.351.4
Missense OE0.89 (0.671.19)
00.61.4
Synonymous OE0.93
01.21.6
LoF obs/exp: 1 / 1.6Missense obs/exp: 32 / 36.1Syn Z: 0.18
DN
0.7034th %ile
GOF
0.77top 25%
LOF
0.1894th %ile

This gene has evidence for multiple mechanisms of pathogenicity (gain-of-function and dominant-negative). Both the Badonyi & Marsh prediction and the broader genomic evidence point to gain-of-function as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

GOFprediction above median
DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TCEAL9 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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