TCEAL8

Chr X

transcription elongation factor A like 8

Also known as: WEX3

This gene encodes a nuclear phosphoprotein that modulates transcription in a promoter context-dependent manner as part of the transcription elongation factor A (SII)-like gene family. Mutations cause X-linked intellectual disability with seizures and behavioral abnormalities. The gene follows X-linked inheritance patterns.

Summary from RefSeq, UniProt
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0
Active trials
0
Pubs (1 yr)
0
P/LP submissions
P/LP missense
1.21
LOEUF
GOF
Mechanism· predicted
Clinical SummaryTCEAL8
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.54) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
1.21LOEUF
pLI 0.543
Z-score 1.42
OE 0.00 (0.001.21)
Moderately constrained

Highly tolerant — LoF variants common in population

Missense Constraint
0.36Z-score
OE missense 0.85 (0.661.11)
40 obs / 46.9 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.00 (0.001.21)
00.351.4
Missense OE0.85 (0.661.11)
00.61.4
Synonymous OE0.88
01.21.6
LoF obs/exp: 0 / 2.3Missense obs/exp: 40 / 46.9Syn Z: 0.38
DN
0.6064th %ile
GOF
0.75top 25%
LOF
0.3549th %ile

The highest-scoring mechanism for this gene is gain-of-function.

GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TCEAL8 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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