TCEAL5

Chr X

transcription elongation factor A like 5

Also known as: WEX4

TCEAL5 encodes a protein containing a BEX domain that may be involved in transcriptional regulation. Mutations cause X-linked intellectual disability with seizures and macrocephaly, following an X-linked inheritance pattern. The gene shows moderate constraint against loss-of-function variants, suggesting intolerance to complete protein loss.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
1
Pubs (1 yr)
76
P/LP submissions
0%
P/LP missense
0.69
LOEUF
Mechanism
Clinical SummaryTCEAL5
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.73) — some intolerance to loss-of-function variants.
📋
ClinVar Variants
74 unique Pathogenic / Likely Pathogenic· 21 VUS of 100 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.69LOEUF
pLI 0.729
Z-score 1.92
OE 0.00 (0.000.69)
Moderately constrained

Typical tolerance to LoF variation

Missense Constraint
1.12Z-score
OE missense 0.66 (0.530.82)
55 obs / 83.9 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.00 (0.000.69)
00.351.4
Missense OE0.66 (0.530.82)
00.61.4
Synonymous OE1.27
01.21.6
LoF obs/exp: 0 / 4.3Missense obs/exp: 55 / 83.9Syn Z: -1.24

ClinVar Variant Classifications

100 submitted variants in ClinVar

Classification Summary

Pathogenic74
VUS21
Likely Benign2
74
Pathogenic
21
VUS
2
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
74
0
74
Likely Pathogenic
0
0
0
0
0
VUS
0
14
7
0
21
Likely Benign
0
1
0
1
2
Benign
0
0
0
0
0
Total01581197

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

TCEAL5 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC