TBX6

Chr 16ADAR

T-box transcription factor 6

Also known as: SCDO5

This gene is a member of a phylogenetically conserved family of genes that share a common DNA-binding domain, the T-box. T-box genes encode transcription factors involved in the regulation of developmental processes. Knockout studies in mice indicate that this gene is important for specification of paraxial mesoderm structures. [provided by RefSeq, Aug 2008]

GeneReviewsOMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

Spondylocostal dysostosis 5MIM #122600
ADAR
0
Active trials
Pubs (1 yr)
P/LP submissions
P/LP missense
0.69
LOEUF
Multiple*
Mechanism· predicted
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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.69LOEUF
pLI 0.007
Z-score 2.57
OE 0.37 (0.210.69)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
0.54Z-score
OE missense 0.91 (0.821.01)
254 obs / 279.2 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.37 (0.210.69)
00.351.4
Missense OE?0.91 (0.821.01)
00.61.4
Synonymous OE?0.98
01.21.6
LoF obs/exp: 7 / 19.1Missense obs/exp: 254 / 279.2Syn Z: 0.17

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TBX6 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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