TASOR2

Chr 10

transcription activation suppressor family member 2

Also known as: C10orf18, FAM208B, bA318E3.2

TASOR2 encodes a core scaffolding component of the HUSH2 complex that mediates epigenetic repression of interferon-stimulated genes through recruitment of other complex members. The gene is highly constrained against loss-of-function variants (LOEUF 0.332), suggesting that mutations would likely cause severe developmental consequences. However, no specific genetic disorders have been definitively associated with TASOR2 mutations to date.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
0
Pubs (1 yr)
25
P/LP submissions
0%
P/LP missense
0.33
LOEUF· LoF intol.
Mechanism
Clinical SummaryTASOR2
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.23) despite low pLI — interpret in context.
📋
ClinVar Variants
25 unique Pathogenic / Likely Pathogenic· 323 VUS of 431 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.33LOEUF
pLI 0.310
Z-score 6.69
OE 0.23 (0.160.33)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
-0.09Z-score
OE missense 1.01 (0.961.06)
1232 obs / 1223.2 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.23 (0.160.33)
00.351.4
Missense OE1.01 (0.961.06)
00.61.4
Synonymous OE1.09
01.21.6
LoF obs/exp: 20 / 87.6Missense obs/exp: 1232 / 1223.2Syn Z: -1.56

ClinVar Variant Classifications

431 submitted variants in ClinVar

Classification Summary

Pathogenic23
Likely Pathogenic2
VUS323
Likely Benign40
Benign1
23
Pathogenic
2
Likely Pathogenic
323
VUS
40
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
23
0
23
Likely Pathogenic
0
0
2
0
2
VUS
0
313
10
0
323
Likely Benign
0
38
0
2
40
Benign
0
0
1
0
1
Total0351362389

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

TASOR2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 2 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found