TAPBP

Chr 6

TAP binding protein

Also known as: MHC1D3, NGS17, TAPA, TPN, TPSN

This gene encodes a transmembrane glycoprotein which mediates interaction between newly assembled major histocompatibility complex (MHC) class I molecules and the transporter associated with antigen processing (TAP), which is required for the transport of antigenic peptides across the endoplasmic reticulum membrane. This interaction is essential for optimal peptide loading on the MHC class I molecule. Up to four complexes of MHC class I and this protein may be bound to a single TAP molecule. This protein contains a C-terminal double-lysine motif (KKKAE) known to maintain membrane proteins in the endoplasmic reticulum. This gene lies within the major histocompatibility complex on chromosome 6. Alternative splicing results in three transcript variants encoding different isoforms. [provided by RefSeq, Jul 2008]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtMHC class I deficiency 3

Clinical highlights

Gene-disease validity (ClinGen)
MHC class I deficiency · ARModerateconsider for supplementary testing
0
Active trials
20
Pubs (1 yr)
P/LP submissions
P/LP missense
1.18
LOEUF
Multiple*
Mechanism· predicted
📖
GeneReview available — TAPBP
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.18LOEUF
pLI 0.000
Z-score 0.95
OE 0.77 (0.511.18)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
0.76Z-score
OE missense 0.87 (0.790.97)
258 obs / 294.9 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.77 (0.511.18)
00.351.4
Missense OE?0.87 (0.790.97)
00.61.4
Synonymous OE?0.89
01.21.6
LoF obs/exp: 15 / 19.5Missense obs/exp: 258 / 294.9Syn Z: 0.98

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TAPBP · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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