TAP2

Chr 6

transporter 2, ATP binding cassette subfamily B member

Also known as: ABC18, ABCB3, APT2, D6S217E, MHC1D2, PSF-2, PSF2, RING11

The membrane-associated protein encoded by this gene is a member of the superfamily of ATP-binding cassette (ABC) transporters. ABC proteins transport various molecules across extra- and intra-cellular membranes. ABC genes are divided into seven distinct subfamilies (ABC1, MDR/TAP, MRP, ALD, OABP, GCN20, White). This protein is a member of the MDR/TAP subfamily. Members of the MDR/TAP subfamily are involved in multidrug resistance. This gene is located 7 kb telomeric to gene family member ABCB2. The protein encoded by this gene is involved in antigen presentation. This protein forms a heterodimer with ABCB2 in order to transport peptides from the cytoplasm to the endoplasmic reticulum. Mutations in this gene may be associated with ankylosing spondylitis, insulin-dependent diabetes mellitus, and celiac disease. Alternative splicing of this gene produces products which differ in peptide selectivity and level of restoration of surface expression of MHC class I molecules. [provided by RefSeq, Feb 2014]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtMHC class I deficiency 2

Clinical highlights

Gene-disease validity (ClinGen)
MHC class I deficiency · ARDefinitivesufficient evidence for diagnostic panels
0
Active trials
38
Pubs (1 yr)
P/LP submissions
P/LP missense
0.79
LOEUF
Multiple*
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.79LOEUF
pLI 0.000
Z-score 2.51
OE 0.52 (0.360.79)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
1.39Z-score
OE missense 0.79 (0.720.87)
281 obs / 354.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.52 (0.360.79)
00.351.4
Missense OE?0.79 (0.720.87)
00.61.4
Synonymous OE?0.94
01.21.6
LoF obs/exp: 17 / 32.4Missense obs/exp: 281 / 354.8Syn Z: 0.58

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

TAP2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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